亚洲制服欧美另类-午夜激情av电影-日本高清中文字幕一区二区三区-中国欧美日韩一区二区三区-欧洲亚洲日本韩国-成人欧美激情一区二区-亚洲偷偷自拍高清

掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
黄 色 网 站 免 费 涩涩屋,国产精品高潮呻吟久久av无码,久久国产精品99精国产
Rabbit Anti-alpha Sarcoglycan/BF350 Conjugated antibody (bs-8740R-BF350)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-8740R-BF350
英文名稱 Rabbit Anti-alpha Sarcoglycan/BF350 Conjugated antibody
中文名稱 BF350標(biāo)記的α肌萎縮糖蛋白2抗體
別    名 50 DAG; 50 kDa dystrophin associated glycoprotein; 50 kDa dystrophin-associated glycoprotein; 50DAG; 50kD DAG; 59kDa; A2; adhalin; ADL; Alpha SG; Alpha-sarcoglycan; Alpha-SG; Asg; DAG2; DMDA2; Dystroglycan 2; Dystroglycan-2; LGMD2D; sarcoglycan, alpha (dystrophin-associated glycoprotein); SCARMD1; Sgca; SGCA_HUMAN.  
規(guī)格價(jià)格 100ul/2980元 購買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 細(xì)胞生物  神經(jīng)生物學(xué)  信號(hào)轉(zhuǎn)導(dǎo)  糖蛋白  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Dog, Pig, Rabbit, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 40kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human alpha Sarcoglycan
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Component of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix.

Function:
Component of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix.

Subunit:
Interacts with the syntrophin SNTA1. Cross-link to form 2 major subcomplexes: one consisting of SGCB, SGCD and SGCG and the other consisting of SGCB and SGCD. The association between SGCB and SGCG is particularly strong while SGCA is loosely associated with the other sarcoglycans (By similarity).

Subcellular Location:
Cell membrane > sarcolemma. Cytoplasm > cytoskeleton.

Tissue Specificity:
Most strongly expressed in skeletal muscle. Also expressed in cardiac muscle and, at much lower levels, in lung. In the fetus, most abundant in cardiac muscle and, at lower levels, in lung. Also detected in liver and kidney. Not expressed in brain.

DISEASE:
Defects in SGCA are the cause of limb-girdle muscular dystrophy type 2D (LGMD2D) [MIM:608099]; also known as Duchenne-like muscular dystrophy autosomal recessive type 2 or severe childhood autosomal recessive muscular dystrophy (SCARMD). LGMD2D is an autosomal recessive degenerative myopathy characterized by progressive muscle wasting from early childhood with loss of independent ambulation by teenage years. Muscle biopsy shows necrosis, decreased immunostaining for alpha sarcoglycan, and adhalin deficiency. The phenotype is less severe than LGMD2C.

Similarity:
Belongs to the sarcoglycan alpha/epsilon family.

Database links:

Entrez Gene: 6442 Human

Entrez Gene: 20391 Mouse

Entrez Gene: 303468 Rat

Omim: 600119 Human

SwissProt: Q16586 Human

SwissProt: P82350 Mouse

SwissProt: Q5SWB2 Mouse

SwissProt: Q28686 Rabbit

Unigene: 463412 Human

Unigene: 18709 Mouse

Unigene: 136653 Rat



Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 a6308.cn 北京博奧森生物技術(shù)有限公司
通過國(guó)際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國(guó)際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
好爽插到我子宫了高清在线 | 热99re久久精品国产首页免 | 黄色的视频在线免费观看 | 久久久久久精品毛片A级按摩 | 日韩成av人片免费观看 | 色综合天天综合欧美综合 | 91无码人妻精品一区 | 玩白嫩少妇小泬高潮18P | 国产精品久久久久久福利 | 欧美BBBBBBSBBBBBB| 97se亚洲综合自在线尤物 | 女人高潮爽到全身痉挛抽搐 | 在线点播亚洲日韩国产欧美 | 蜜桃网站入口可看18禁 | 国产精品一区二区AV交换 | 理论片午午伦夜理片影院99 | 亚洲色欲色欲WWW在线丝 | 国内精品久久久久影视老司机 | 国产97人人超碰cao蜜芽国产 | 牛牛影视午夜免费福利 | 在线A亚洲老鸭窝天堂AV高清 | 动漫美女h片黄动漫在线观看 | 亚洲国产欧美中日韩成人综合视频 | 免费在线视频一区 | 无码精品人妻一区二区三区免费 | 欧美又大又粗又硬BBBBB小说 | 日本不卡一区二区三区 | 欧美韩国人成网站中文字幕 | 全黄裸片一29分钟免费真人版 | 久久久久人妻精品一区5555 | 中文字幕不卡一区二区三区 | 二区久久久国产AV色 | 日本BBW丰满牲交片 国产精品国产三级国产AV剧情 | 好吊妞视频这里有精品 | 欧美亚洲日本一区 | 向日葵视频APP秋葵榴莲在线 | 久久精品自慰喷水一区二区下载 | 老头埋进校花里面使劲添 | 超清无码A片在线观看不卡 大乳妇女BD丰满 | 国产成人精品久久一区二区三区 | 久青草国产97香蕉在线视频 |